Prenatal diagnosis of an isolated coronary arterial fistula.

Congenital coronary artery fistulas (CAF) are rare malformations which can be complicated by hemodynamically relevant intracardiac shunts, endocarditis, myocardial infarction, thromboemboly or coronary aneurysms and rupture. The incidence of isolated coronary fistula is 1:50000 live birth (Schumacher G et al. Thorac Cardiovas Surg 1997; 45: 287–294). The left, right or both coronary arteries may be involved. The fistulas drain mainly to the right heart side (92 %) with 41 % to the right ventricle (Schumacher G et al. Thorac Cardiovas Surg 1997; 45: 287–294). We report the exceptional prenatal diagnosis of a fistula of the left coronary artery to the right ventricle at 26 weeks of gestation.